Abstract
No single surgical procedure for total colonic aganglionosis (TCA) has clearly been proven to be superior. Experiences and long-term results of a standard Duhamel pull-through procedure in the management of this rare form of Hirschsprung's disease are presented. Thirty-six cases with Hirschsprung's disease were retrospectively reviewed, 12 (31.4%) of whom had TCA. All operated patients with TCA had a diversion in the first week of life. Duhamel's procedure was the definitive procedure for all patients and was performed between 6 months and 1 year of age. All patients were followed-up for between 30 months and 21 years. Incontinence was assessed on the basis of soiling in the diaper between 2 consecutive defecations in the younger group and the need for a diaper in the older age group. Hirschsprung's enteritis was regarded severe if the patient's condition did not improve on conservative management and the patient needed an ileostomy post–pull-through. Half of the patients have an almost normal number of daily bowel movements. It is concluded that the long-term results of a standard Duhamel's pull-through for TCA are good in continence, bowel motions, and physical development.
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
