Y-type urethral duplication: A case series of four cases with good outcome

Abstract

Urethral duplication is a rare congenital condition. This case series intends to strengthen the concept of Y-type urethral duplication (new anatomic variation of an accessory limb of duplicated urethra). We have conducted a retrospective analysis collecting information from four cases of type IIA-2Y variety of urethral duplication (Effmann classification), which is one of rarely found subtype with its embryogenesis, diagnosis and single stage repair with outcome. Four babies around 1- 6 months of age range (mean- 3.2 months), complaining of passing urine from a site other than penis which includes anal canal, perineal area. All babies were investigated for other associated anomaly and were planned for surgery. Three out of four cases had undergone excision of accessory urethra and urethral stent in ventral urethra in postoperative period for 8-10 days with good results. In one case, posterior sagittal anorectoplasty ( PSARP ) approach was used to delineate accessory urethra and end to end urethral anastomosis was done with better outcome. All babies are on regular follow up till now ranging 6months to three years. It is important to delineate the functional urethra before planning for intervention so as to address the problem.