Wunderlich Syndrome: A Rare Case Associated with Bleeding Renal Angiomyolipoma (AML).

Abstract

Renal angiomyolipoma (AML) is a benign mesenchymal tumor composed of fat, smooth muscle, and blood vessels. It represents 1-3% of solid renal tumors. Despite the benign nature of this tumor, it can be aggressive with locoregional extension. We describe a case of a 60-year-old female who presented with left flank pain and unstable blood pressure. A CT scan showed a renal mass with hemorrhagic densities. Peroperatively, bleeding from the renal mass was revealed, and the patient underwent radical nephrectomy. A myriad of symptoms such as acute flank pain, flank mass, and bleeding led to the diagnosis of Wunderlich syndrome, which is usually seen secondary to AML and renal cell carcinoma. Histopathologic examination helped in arriving at the diagnosis of renal AML with secondary changes, ruling out malignancy. Early diagnosis and immediate intervention saved her life and reduced morbidity. This case report helps in sensitizing clinicians and thus facilitates the detection of similar cases at the earliest.