Wegener's granulomatosis with bilateral facial nerve paresis and bilateral profound sensorineural hearing loss

Abstract

Wegener's granulomatosis (WG) is a fatal disease. Facial nerve paralysis in association with WG is rare, being present in about 5% of patients, alone or in combination with hearing loss and rarely may be the only presenting feature. We are reporting a case of WG presenting with bilateral facial paresis and its peculiarity consists in its acute onset, lack of a significant previous history of ear disease and its association with bilateral profound sensorineural hearing loss. A Medline search revealed that there has been no reported case of WG presenting with bilateral facial involvement with bilateral profound sensorineural hearing loss.