Visual Loss After Retrogasserian Glycerol Injection

Abstract

and multiple spontaneous joint dislocations (Fig. 2). Slit-lamp examination showed punc­ tate staining and neovascularization of the infe­ rior one third of both corneas caused by sponta­ neous bilateral entropion of the lower eyelids and extreme laxity. She was treated with lateral tarsorrhaphies in both eyes, which decreased the corneal exposure and corrected the entropi­ on. Larsen's syndrome is a rare condition with severe orthopedic abnormalities. The affected individuals have a pathognomonic cylindrical shape to their fingers, which do not taper distal­ ly. Additionally, they have spatulate thumbs and short metacarpals. Only the major joints spontaneously dislocate; the shoulder, wrist, and fingers are not involved. The bone develop­ ment is normal as is the dentition; however, cleft palate, cleft uvula, or midline uvular groves have been reported. The flattened facies is accentuated by the prominent forehead and depressed nasal bridge. In this patient, the flat facies and marked cutaneous laxity contributed to the spontane­ ous entropion and subsequent keratopathy. Fortunately, both of these conditions were cor­ rected by lateral tarsorrhaphies.