Very Rare Cause of Fixed Obstruction and Severe Asthma: A Case with Keutel Syndrome

Abstract

Keutel syndrome is rare inherited disorder with mutations in the matrix G1a protein (MGP). Most of the patient is diagnosed in early childhood. They admitted to the hospital due to hearing loss, recurrent upper respiratory tract infections, chronic cough. In this case report Keutel syndrome is discussed in an adult patient.