Vasculitis in primary Sjögren’s syndrome

Abstract

Sjogren’s syndrome (SS) is a chronic autoimmune disease, characterized by lymphocytic infiltration of the exocrine glands resulting in xerostomia and keratoconjunctivitis sicca. These manifestations can occur al.one (primary SS) or in association with other autoimmune disorders, such as rheumatoid arthritis or systemic lupus erythematosus (secondary SS). Extraglandular manifestations are seen in approximately half of SS patients and include Raynaud’s phenomenon, splenomegaly, lymphad-enopathy, lung involvement, kidney involvement, liver involvement and vasculitis [1].