Vaginoscopic Resection of Oblique Vaginal Septum in OHVIRA Syndrome Before Menarche

Abstract

To demonstrate vaginoscopic resection of the oblique vaginal septum in a girl with Obstructed Hemi Vagina and Ipsilateral Renal Agenesis (OHVIRA) syndrome, before menarche. Stepwise demonstration of surgical technique with narrated video footage. OHVIRA syndrome is a rare urogenital anomaly in which the patients present after menarche, with progressive dysmenorrhea and a palpable pelvic mass due to hematocolpos and hematometra on the obstructed side. Delay in diagnosis may cause endometriosis, pelvic adhesions, and infertility (1)(2). A 12-year-old, premenarchal girl with complaints of pelvic pain and an ultrasound report of right renal agenesis was referred to the urology department of our hospital. She was also found to have uterus didelphys and a loculated fluid collection behind the urinary bladder on ultrasonography and on MRI (Figure 1 & 2). A probable diagnosis of OHVIRA syndrome with mucocolpos was made (3). Vaginoscopy showed an obstructing bulging vaginal septum on the right side. The left uterine horn was inspected by hysteroscopy. The vaginal septum was incised vaginoscopically with monopolar cautery using Collins knife(4)(5)(6). The collected mucus was drained. Right cervix and the right uterine horn were visualized by hysteroscopy. Edges of the septum were resected with a resectoscope loop. The hymen was not injured during the surgery. Relook vaginoscopy done after two months showed a normal and healed vagina. Vaginoscopic resection of the obstructing oblique vaginal septum in OHVIRA syndrome is a very simple, minimally invasive and a virginity conserving surgery. Early diagnosis and treatment can prevent future complications due to cryptomenorrhea.