Uterine tumor resembling ovarian sex cord tumor: we can diagnose it if we consider it. Case report and literature review

Abstract

Uterine tumor resembling ovarian sex cord tumor (UTROSCT) represents a rare uterine neoplasm with un­certain malignant potential. Several reports have described re­cur­rences, me­tas­ta­ses and even deaths associated with these generally considered benign tumors, thus making them a controversial disease entity. UTROSCT has an un­clear histogenesis and it possesses a polyphenotypic im­mu­no­phe­no­type. We present a case of UTROSCT in a patient accusing ab­nor­mal genital bleeding and symptoms associated with anemia. After per­for­ming a total abdominal hysterectomy with bilateral sal­pin­gec­tomy, the final pathology report revealed UTROSCT with no sarcomatous features. The pa­tient is still disease-free after 30 months of follow-up. We also present the data avai­la­ble in literature regarding this relative new type of uterine tu­mor. We are of the opinion that a high index of suspicion is of paramount importance when examining a patient with an uterine mass in order to promptly identify the risk factors that may predict agressive tumor behaviour.