Uterine didelphys with duplicated upper vagina and bilateral lower vaginal agenesis: a novel Müllerian anomaly with options for surgical management

Abstract

To describe a novel Müllerian anomaly and management options. Case series report. Metropolitan tertiary care children's hospital. Three caucasian girls, aged 12, 13, and 15 years, with a novel congenital anomaly. Interval staged vaginoplasties. Functional vagina. Didelphys Müllerian development with vaginal duplication and agenesis of both lower vaginas with staged vaginoplasties resulting in normal functional vaginas. Staged pull-through vaginoplasties led to functional outcome in this unusual anomaly.