Abstract
Idiopathic Pulmonary Haemosiderosis (IPH) is a rare disease commonly affecting the paediatric population with approximately 500 globally reported cases in the literature. The disease usually presentswith a symptom triad consisting of ferropenic anaemia, cough with haemoptysis and diffuse bilateral alveolar infiltrates. Therapeutic options for this disorder are not only limited but also not fully effective. Moreover, corticosteroids remain the mainstay of IPH treatment. This communication reviews the available evidence in support of corticosteriod usage in the treatment of IPH. We conclude that the use of corticosteroid in IPH treatment is unfathomed and demands further investigation.
Highlights
Idiopathic Pulmonary Haemosiderosis (IPH) is a rare disease commonly affecting the paediatric population with approximately 500 globally reported cases in the literature
Various therapeutic modalities have been tried for IPH including the use of inhaled and systemic corticosteroids, administration of immunosuppressant drugs and blood transfusions
According to a case report, corticosteroid therapy has been effective in preventing the episodes of haemoptysis in a patient who was initially maintained on a 20mg dose of prednisolone that was tapered to 10mg dose of the drug one month later.[10]
Summary
Idiopathic Pulmonary Haemosiderosis (IPH) is a rare disease commonly affecting the paediatric population with approximately 500 globally reported cases in the literature.
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