Unusual Torsion of Hematosalpinx in a Case of MRKH Syndrome

Abstract

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital anomaly of the female reproductive tract characterized by the absence of the upper two thirds of the vagina and the uterine cervix, and hypoplasia or complete aplasia of the uterus [1]. Typically, patients with MRKH syndrome present with primary amenorrhea while exhibiting normal secondary sexual characteristics and a normal female karyotype (46, XX) [2]. In fewer cases, they suffer from cyclic pelvic pain due to active endometrium in the hypoplastic uterine horns [3].