Unusual longevity in a patient with factor X Friuli coagulation disorder

Abstract

Longevity is rare in congenital bleeding disorders. In the past, brain hemorrhages were the main cause of death, while AIDS and liver failure related to post-transfusion, hepatitis B or C have now become the major causes of death. Most data on causes of death refer to hemophiliacs and to von Willebrand disease (1-5). Information on rare coagulation disorders is scarce. This report was prompted by the opportunity to follow a group of patients with FX Friuli disorders for approximately 35 years, and the observation that one of these patients is alive and well at the age of 102. . . .