Unusual lingual-mandibular continuous myoclonus

Abstract

Lingual-mandibular myoclonus is a very unusual movement disorder. We report a very unusual case of continuous myoclonus invloving the tongue in a 34 years old patient. She is a case of cerebral palsy with undetermined etiology and she developed right anterior cerebral infarction. Consecutively she started to have rhythmic and persistent rythmic abnormal movements involving the tongue and the jaw in the same time. Her Imaging studies including brain CT scan, MRI and MRA showed occlusion of the right anterior cerebral artery with infarction in whole its territory.The abnormal movements subsided near completely on Depakine PO. The EEG monitoring failed to show epileptiform discharge. The pathophysiology of this exceptionally rare abnormal movements involving both the tonguye and the jaw is discussed. This is a very unusual presentation of abnormal movement responding to Depakine.