Abstract

Abbreviations/Acronyms: AiCL, autoinflammatory chilblain lupus; AID, autoinflammatory diseases; AiG, autoinflammatory granulomatosis; HS, hidradenitis suppurativa; I&D, incision and drainage; IBD, inflammatory bowel disease; IEI, inborn error of immunity; ILD, interstitial lung disease; IVIG, intravenous immunoglobulin; MRSA, methicillin-resistant Staphylococcus aureus; PAC, pyoderma gangrenosum, acne and ulcerative colitis; PAPA, pyogenic arthritis, pyoderma gangrenosum and acne conglobata; PAPASH, pyoderma gangrenosum, acne, suppurative hidradenitis and pyogenic arthritis; PASH, pyoderma gangrenosum, acne, and suppurative hidradenitis; PASS, pyoderma gangrenosum, acne conglobata, suppurative hidradenitis and axial spondyloarthritis; PGAAIS, pyoderma gangrenosum-associated autoinflammatory syndromes; PsAPASH, pyoderma gangrenosum, acne, suppurative hidradenitis and psoriatic arthritis; UUAiD, ulcerative undefined autoinflammatory disease

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