Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report

Abstract

Correspondence address: Mario Luiz Ribeiro Monteiro. Neuro-Ophthalmology Service. Escola de Me dicina da Universidade de Sao Paulo. Av. Angelica, 1.757 Conj. 61 Sao Paulo (SP) 01227-200 Brazil E-mail: mlrmonteiro@terra.com.br I read with interest the report of “Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report” by Apostolos-Pereira et al. Central retinal artery occlusion is very rare in Susac syndrome as evidenced by the paucity of reports in the clinical literature. The corpus callosum findings in this case are pathognomonic for the disease with the central callosal lesion and the 2 small spoke lesions in the posterior callosum. However, the fundus appearance is somewhat odd with the significant platelet-like embolic material in the arterioles. These are not Gass plaques as has been described previously. Did they disappear after his initial presentation? There are also characteristic fluorescein angiographic findings described previously. Was the typical autofluorescense pattern located remotely from the retinal artery occlusion? I am particularly interested in learning if the right eye showed this pattern prior to infarction; if so, can this be published? Were anti-en dothelial cell antibodies sent?