Un cas de syndactylie bilatérale complexe, complète et compliquée

Abstract

We report the case of a 21-year-old female patient, born with a bilateral hand deformity consisting of syndactyly of the 3rd and 4th rays on each side, without any other associated congenital anomaly. In order to correct the functional and aesthetic discomfort caused by this malformation, she consulted an orthopedic surgeon. A hand X-ray (A, B) was performed to determine the type of syndactyly and any associated bony hand anomalies. It revealed a complex, complete and complicated bilateral syndactyly with, on both the right and the left, a bifidity of the phalanges of the 4th ray forming a synostosis with the 3rd ray. The rest of the bones and joints of the hand are normal. Syndactyly is one of the most common congenital anomalies of the extremities. It is a defect in finger differentiation, defined as a fusion of adjacent fingers. Syndactyly can be seen in the upper and lower extremities, and up to 50% of cases are bilateral. To avoid the morbidity associated with this condition, it must be diagnosed and treated promptly. Syndactyly is described as simple or complex, depending on the presence (complex) or absence (simple) of bony fusion. Complete syndactyly extends to the fingertips with inclusion of the nail folds, while incomplete syndactyly does not extend the full length of the finger. Complicated syndactyly is defined by the presence of interposed accessory phalanges or abnormal bones.