Ultrasound Guided Supraclavicular Block in Poland Syndrome : A Safe Alternative to General Anaesthesia

Abstract

Poland syndrome is an uncommon, congenital anomaly characterized by multiple systems and organs involvement like musculoskeletal, lungs, heart, kidneys and haemopoetic system with absence of functional disability. Right sided Thorax deformity is the most common feature of this syndrome with the absence of underlying bones and muscles making this condition similar to open chest along with ipsilateral hand anomalies such as brachydactyly, syndactyly or ectodactyly [1]. The incidence of this syndrome is 1 per 30,000-50,000 live births [2]. Patients with Poland syndrome require anesthesia during surgical procedures to correct the associated deformities or the organ systems associated with the disease process. Literature shows that these patients may be more susceptible for malignant hyperthermia due to associated musculoskeletal abnormalities under general anesthesia [3]. Moreover respiratory problems and hypoxia in the perioperative period may be related to associated paradoxical breathing, lung hypoplasia and chest wall abnormalities in otherwise asymptomatic patient at rest. We report a diagnosed case of Poland syndrome presented for syndactly release Keywords: USG blocks, Supraclavicular approach.