Abstract
Tumor fibroso solitário extrapleural (TFS) é neoplasia mesenquimal rara, sendo que há menos de 40 casos descritos com localização em extremidades até o presente momento. Acomete preferencialmente pacientes na quinta década e não tem predileção por sexo. Relatamos um caso com os aspectos clínicos, radiológicos, histológicos e imunoistoquímicos característicos, discutindo a importância do diagnóstico diferencial com outros sarcomas.Pouco é conhecido sobre o comportamento biológico do TFS. Fatores de risco para menor sobrevida livre de metástases incluem: margens cirúrgicas comprometidas, tamanho maior que 10 cm e histologia maligna. Excisão completa é o tratamento recomendado.
Highlights
Extrapleural solitary fibrous tumor (SFT) is a rare mesenchymal neoplasm, with less than 40 cases reported affecting the extremities so far
Extrapleural solitary fibrous tumor (SFT) is a mesenchymal tumor of probable fibroblastic type with presence of vessels exhibiting a branching pattern that resembles that of hemangiopericytoma.[1,2]
There are fewer than 40 cases described in literature in soft parts of extremities.[1,3]
Summary
Extrapleural solitary fibrous tumor (SFT) is a rare mesenchymal neoplasm, with less than 40 cases reported affecting the extremities so far. There are fewer than 40 cases described in literature in soft parts of extremities.[1,3] The vast majority are benign and cured by simple complete excision of the lesion.
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