Treinamento muscular respiratório em Distrofia Muscular de Duchenne: série de casos

Abstract

The weakness of the respiratory muscles is the main responsible for respiratory failure in Duchenne Muscular Dystrophy (DMD). Objec­tive. Evaluate the effects of inspiratory muscle training on respiratory strength in patients with DMD. Method. A clinical trial of single group of five children with DMD, aged 11.4±2.6 years, assessed by Manovacuometry and Peak Expiratory Flow (PEF) for the initial time (baseline), fifth and tenth session . Held inspiratory muscle training, with 30% of PImax in linear load (Threshold®) device with five sets of 10 repetitions, totaling 10 sessions, three times a week. Results. Mean values initial, fifth and 10th session, respectively: PImax (cmH2O): -64 , -69.8 and -86.8 (p=0.006) improvement of 29% in 10 sessions; PEmax (cmH2O) : 64 , 67 and 73.6 (p=0.003) improvement of 25% in 10 sessions and PEF (L/min): 210 , 218 and 232 (p=0.012) im­provement of 9% in 10 sessions. Conclusion. The inspiratory muscle training program proposed proved to be effective in both the inspi­ratory and expiratory force gain, providing also the increased peak expiratory flow.