Abstract
Behçet’s disease (BD) is a multisystemic vasculitis of unknown etiology. Cardiovascular involvement has been thoroughly described in the literature and the major cause of death in BD is secondary to aneurysm complications. In this case report, a patient with BD presented with a recurrent abdominal aortic aneurysm, which was corrected using a custom-made endoprosthesis. The optimal treatment for patients with BD remains highly controversial and challenging because of technical difficulties and frequent recurrence. Endovascular intervention seems to be a feasible alternative with considerably less morbidity than conventional surgery.
Highlights
Behçet’s disease (BD) is a multisytemic vasculitis first described in 1937 by Hulusi Behçet, characterized by a triad comprising recurrent aphthous stomatitis, genital ulceration, and refractory uveitis.[1]
There is an international criterion for diagnosis/classification of BD, based on a scoring system that attributes two points each to ocular lesions and genital ulcers and one point to each of the following items: oral apthous ulcers; cutaneous manifestations; vascular manifestations; and a positive pathergy test
Three or more points are needed to define a patient as a case of BD.[5]
Summary
Sergio Quilici Belczak1,2 , Ingredy Tavares da Silva[1], Gustavo Garcia Marques[1], Letícia Flores Copetti[1], Vanessa Stefaniak[1], Gustavo Gomes Quintas[1], Kaique Bernardo Uchimura[1]
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