Transverse myelitis presenting in a patient with Hughes-Stovin syndrome

Abstract

Hughes-Stovin syndrome (HSS) is a lymphocytic vasculitis defined by the constellation of venous thrombosis and multiple pulmonary artery aneurysms. Aneurysmal rupture with massive hemorrhage is a frequent fatal event. HSS is thought of as a forme fruste of Behcet's disease (BD), sharing similar histological findings, but without other associated manifestations that characterize BD. Classically patients with HSS do not have oral and genital ulcers, inflammatory eye disease, skin pathergy, nor do they develop neurological manifestations that can arise with