Total anomalous systemic venous drainage with heterotaxia syndrome: a rare case.

Ali Yildirim,Birsen Ucar,Gokmen Ozdemir,Zubeyir Kilic,Pelin Kosger

doi:10.1155/2014/392841

Abstract

Total anomalous systemic venous return is a very rare anomaly, where vena cava inferior, vena cava superior, and coronary sinus drain into left atrium. Two-day-old male baby was admitted with cyanosis and tachypnea after the birth. Left atrial isomerism with anomalous systemic venous drainage was found on echocardiographic examination. We present an unusual case of total anomalous systemic venous drainage in to the left atrium.

Highlights

Total anomalous systemic venous return is a very rare anomaly, where vena cava inferior (IVC), vena cava superior (SVC), and coronary sinus drain into left atrium [1]
We present a case of left atrial isomerism with anomalous systemic venous drainage, in a 2-day-old male patient
Total anomalous systemic venous return cases are scarce in the literature [2]

Summary

Introduction

Total anomalous systemic venous return is a very rare anomaly, where vena cava inferior (IVC), vena cava superior (SVC), and coronary sinus drain into left atrium [1]. We present a case of left atrial isomerism with anomalous systemic venous drainage, in a 2-day-old male patient. There are few published reports regarding the total anomalous systemic venous drainage with heterotaxy syndrome

Case Report

Findings

Discussion