Abstract
Thoracoschisis is a rare condition. A female newborn presented with right-sided thoracoschisis, associated with diaphragmatic hernia and protrusion of an accessory liver lobe through the chest wall defect along with deformity of the right forearm and hand duplication. Diagnosed as part of the limb-body wall complex (LBWC), management included resection of the exteriorized liver lobe followed by right hemidiaphragm and thoracic wall reconstruction.
Highlights
Thoracoschisis is a rare congenital anomaly that usually presents an evisceration of organs through a lateral chest wall defect [1]
Thoracoschisis is an extremely rare congenital anomaly. In this condition there is thoracic wall defect lateral to the midline, through which liver and intestine can herniated after passing through the diaphragmatic defect on the same side
The liver lobe that exteriorizes throughout the thoracic wall defect is an accessory Riedel lobe
Summary
Thoracoschisis is a rare congenital anomaly that usually presents an evisceration of organs through a lateral chest wall defect [1]. It is often associated with a diaphragmatic hernia, defect of the anterior abdominal wall and limb malformation, the so-called "limb-body wall complex" (LBWC) deformity [2]. We are reporting a case of thoracoschisis associated with LBWC.
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