Abstract
ObjectiveThis study sought to summarize the clinical experience of surgical treatment of anomalous origin of pulmonary arteries from the ascending aorta (AOPA) in Fuwai hospital.MethodsFifty-two patients (28 males, 17.2 ± 27.2 months old and 8.7 ± 10.2 Kg weight) who have AOPA undertook surgical treatment between 1998 and 2017 were reviewed in this study, 47 out of 52 are anomalous origin of the right pulmonary artery (AORPA), among the rest of the patients are anomalous origin of left pulmonary artery (AOLPA). 27 out of 52 associate with simple cardiac abnormalities, 20 out of 52 associate with complex cardiac malformations, the remaining 5 patients without cardiac abnormalities. Among all patients who underwent surgical treatment, the direct end-to-side anastomosis strategy was applied in 26 patients, autologous pericardial-homograft patch and aortic flap were employed in 20 patients, and synthetic graft was used in 6 patients.ResultsNo patient died during the perioperative period. 50 out of 52 patients were followed-up for 100.1 ± 70.9 months. The rate of pulmonary arterial free restenosis for 2 years, 5 years, and 10 years is 98.0, 96.0 and 92.0%, respectively.ConclusionsThe correct diagnosis and appropriate surgical treatment for AOPA could obtain excellent early and medium-term result.
Highlights
Anomalous origin of pulmonary arteries from the ascending aorta (AOPA) is a rare congenital heart disease. It is known as hemi-truncus, anomalous origin of the right pulmonary artery (AOPRA) is more commonly than anomalous origin of the left pulmonary artery (AOPLA)
16 patients underwent angiography, Dong et al Journal of Cardiothoracic Surgery (2019) 14:82 and 9 patients underwent cardiac computed tomography (CT) examination. 47 patients had an abnormal right pulmonary artery originating from the ascending aorta and 5 patients had an abnormal left pulmonary artery originating from the ascending aorta
According to Kutsche’s classification [2], 48 cases were proximal type and 4 cases were distal type. 33 cases associate with patent ductus arteriosus, 20 cases associate with atrial septal defect, 7 cases associate with ventricular septal defect, 4 cases associate with tetralogy of Fallot (4 cases of abnormal origin of left pulmonary artery), 8 cases associate with aortic-pulmonary window, and 5 cases associate with interruption of aortic arch; 5 cases did not associate with deformity
Summary
Anomalous origin of pulmonary arteries from the ascending aorta (AOPA) is a rare congenital heart disease. It is known as hemi-truncus, anomalous origin of the right pulmonary artery (AOPRA) is more commonly than anomalous origin of the left pulmonary artery (AOPLA). Pulmonary arteries originating from the ascending aorta produces a large amount of left-to-right shunt, which leads unilateral lung to receive systemic circulatory pressure. General information We retrospectively analyzed the clinical data of 52 cases of pulmonary arterial abnormalities originating from ascending aorta during surgery between 1998 and 2017 in our hospital, There are 28 males and 24 females (Table 1); the mean age at the operation was 17.2 months (8 days to 19 years old). 3 case’s diagnosis were missed before operation, no angiography or CT examination were performed before operation
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
