The spectrum of the visual field defects in the tilted disc syndrome Clinical study and review

Abstract

The tilted disc syndrome is a common ocular anomaly characterized by dysversion of the optic disc, congenital crescent, situs inversus of the retinal vessels, and ectasia and depigmentation of the fundus. The anomaly causes visual field defects that can mimic the defects produced by other neuro-ophthalmological diseases, particularly chiasmal lesions. This paper deals with the visual field defects of the tilted disc syndrome in an attempt to classify them and to find differential features as regards similar defects of other origin. Four types of visual field were charted in patients with tilted disc syndrome: normal field, altitudinal, quadrantanopia-like and hemianopia-like defects. These latter two defects tend to cross the vertical meridian, point towards the blind spot, and are partly surrounded by an arc of vision. A correspondence exists between the type of visual field defect and the position of the depigmented/ectatic area of the fundus.