Abstract
In this article, we describe the role of radiology for diagnosis and follow-up of progressive fibrosing interstitial lung disease (PF-ILD). Patients with PF-ILD are at increased risk for early death without treatment. Clinical diagnosis of PF-ILD has been described in the literature. This manuscript reviews the radiographic diagnosis of PF-ILD and the unique CT characteristics associated with specific types of fibrosis. Ultimately, we believe that radiology has the potential to recognize progression early and thus make an important contribution to the multidisciplinary discussion for this important diagnosis.
Highlights
The Role of Radiology in Progressive Fibrosing Interstitial Lung DiseaseSpecialty section: This article was submitted to Pulmonary Medicine, a section of the journal
In broad terms, there are two types of interstitial lung diseases (ILDs); one of which is primarily inflammatory with the potential for complete resolution but with the possibility of transformation into a fibrotic phenotype, the other is a primarily fibrotic ILD and largely irreversible [1]
We reviewed 103 patients with a working diagnosis of idiopathic pulmonary fibrosis (IPF), 68 had a probable USUAL INTERSTITIAL PNEUMONITIS (UIP) pattern on the initial CT, 47% progressed to a UIP pattern with honeycombing (HC) over 51 months, having a progressive phenotype
Summary
Specialty section: This article was submitted to Pulmonary Medicine, a section of the journal
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