Abstract
BackgroundThe Japan Renal Biopsy Registry (J-RBR), the first nation-wide registry of renal biopsies in Japan, was established in 2007, and expanded to include non-biopsy cases as the Japan Kidney Disease Registry (J-KDR) in 2009. The J-RBR/J-KDR is one of the biggest registries for kidney diseases. It has revealed the prevalence and distribution of kidney diseases in Japan. This registry system was meant to be revised after 10 years.MethodsIn 2017, the Committees of the Japanese Society of Nephrology started a project for the revision of the J-RBR/J-KDR. The revised system was designed in such a way that the diagnoses of the patients could be selected from the Diagnosis Panel, a list covering almost all known kidney diseases, and focusing on their pathogenesis rather than morphological classification. The Diagnosis Panel consists of 22 categories (18 glomerular, 1 tubulointerstitial, 1 congenital/genetical, 1 transplant related, and 1 other) and includes 123 diagnostic names. The items for clinical diagnosis and laboratory data were also renewed, with the addition of the information on immunosuppressive treatment.ResultsThe revised version of J-RBR/J-KDR came into use in January 2018. The number of cases registered under the revised system was 2748 in the first year. The total number of cases has reached to 43,813 since 2007.ConclusionThe revised version 2018 J-RBR/J-KDR system attempts to cover all kidney diseases by focusing on their pathogenesis. It will be a new platform for the standardized registration of kidney biopsy cases that provides more systemized data of higher quality.
Highlights
The Japan Renal Biopsy Registry (J-RBR), the first nationwide web-based registry of renal biopsies in Japan, was established in 2007 [1]
Progressive Nephritic Syndrome, rapidly progressing renal failure within several weeks to several months that is associated with urinary findings, such as proteinuria, hematuria, red blood cell casts, and granular casts indicating glomerulonephritis [28]
The clinical diagnoses of the patients are selected from the list shown in Fig. 1, which includes urinary abnormalities, acute nephritic syndrome, chronic nephritic syndrome, rapidly progressive nephritic syndrome, nephrotic syndrome, acute kidney injury (AKI), chronic kidney dysfunction, and others
Summary
The Japan Renal Biopsy Registry (J-RBR), the first nationwide web-based registry of renal biopsies in Japan, was established in 2007 [1]. J-RBR Japan Renal Biopsy Registry, J-KDR Japan Kidney Disease Registry, RPGN rapid progressive glomerulonephritis, CRF chronic renal failure, CKD chronic kidney disease, DM diabetes mellitus, AKI acute kidney injury, FSGS focal segmental glomerulosclerosis, ANCA anti-neutrophil cytoplasmic antibody, MPO myeloperoxidase, PR3 proteinase 3, EUVAS the European Vasculitis Study Group, GBM glomerular basement membrane, ISKDC the International Study of Kidney Disease in Children, ISN/RPS the International Society of Neurology and the Renal Pathology Society, UPCR urinary protein creatinine ratio, RBC red blood cell, HPF hyper power field, CRP C-reactive protein, NGSP the National Glycohemoglobin Standardization Program, HBV hepatitis B virus, HCV hepatitis C virus, HIV human immunodeficiency virus it provides essential information for managing the condition [2,3]. It will be a new platform for the standardized registration of kidney biopsy cases that provides more systemized data of higher quality
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