The Perioperative Management of a Patient With Fontan Physiology for Pheochromocytoma Resection

Abstract

ADULTS WITH CONGENITAL HEART DISEASE (CHD) are a growing population. In 2000, about 1.2 million adults were living in the United States with various forms of CHD. 1 Warners C.A. Liberthson R. Danielson Jr, G.K. et al. Task Force 1: The changing profile of congenital heart disease in adult life. J Am Coll Cardiol. 2001; 37: 1170-1175 Abstract Full Text Full Text PDF PubMed Scopus (1073) Google Scholar Approximately 85% of babies born with CHD may reach adulthood and may require noncardiac surgery. Pheochromocytoma resection has been reported in patients with single ventricle and a Blalock-Taussig shunt 2 Tjeuw M. Fong J. Anaesthetic management of a patient with a single ventricle and phaeochromocytoma. Anaesth Intensive Care. 1990; 18: 567-569 PubMed Google Scholar or a combined cavopulmonary anastomosis/central shunt. 3 Sparks J.W. Seefelder C. Shamberger R.C. et al. The perioperative management of a patient with complex single ventricle physiology and pheochromocytoma. Anesth Analg. 2005; 100: 972-975 Crossref PubMed Scopus (18) Google Scholar The authors report the perioperative management of a patient with a pheochromocytoma and a Fontan repair.