The Effectiveness of Cochlear Implants in Patients with Inner Ear Malformation

Lina Alefranji

doi:10.19080/gjo.2021.24.556129

Abstract

The Effectiveness of Cochlear Implants in Patients with Inner Ear Malformation

Highlights

Cochlear implant (CI) is a surgical solution for patients who suffer from unilateral or bilateral severe to profound sensorineural hearing loss (SNHL) and is one of the most challenging ear surgeries as it needs a highly professional surgeon to perform it
The engine search showed a total of 799 related studies, out of which we found sixty-four studies that fulfill the inclusion criteria and are related to the outcome of a CI with inner ear malformations (IEM)
The studies have included a total of 17636 CI subjects including 2836 (16%) cases who were diagnosed with IEM with this being categorized into: (n=947) enlarged vestibular aqueduct at 33%, (n=153) common cavity at 5%, (n=135) cochlear hypoplasia at 5%, (n=102) incomplete partition “unclassified” at 4%, (n=156) incomplete partition type I at 6%, (n=680) incomplete partition type Incomplete Partition Type II (II) “Mondini” at 24%, (n=26) incomplete partition type Incomplete Partition Type III (III) at 1%, (n=637) other malformations at 22% including single or multi malformations

Summary

Introduction

Cochlear implant (CI) is a surgical solution for patients who suffer from unilateral or bilateral severe to profound sensorineural hearing loss (SNHL) and is one of the most challenging ear surgeries as it needs a highly professional surgeon to perform it. This is especially the case for patients who have inner ear malformations (IEM), facial nerve abnormalities, cerebrospinal fluid leakage (CSF), gusher, or difficulty in finding the cochlea itself. The most common classification that has been used to determine the IEM is Jackler et al who classified the IEM into five categories and Sennaroğlu & Bajin [5] who classified the inner ear anomalies into eight categories (Table 1)

Methods

Results

Discussion

Conclusion