Abstract
Aim. Echocardiography has become the main mean in detection of noncompaction cardiomyopathy (NCC). However, misdiagnosis and missed diagnosis were common. The aim of this paper was to analyze the misdiagnosis and missed diagnosis of NCC, improve the diagnostic accuracy of this disease. Material and methods. We retrospectively analyzed the data of 56 subjects who had been clinically diagnosed with NCC in our institution, which included patients’ total echocardiographic data since the disease onset. Echocardiographic data and cardiac magnetic resonance (CMR) data were compared with each other. Results. 17 of the total subjects had been diagnosed with NCC after the first echocardiography at our institution. 39 subjects had not been diagnosed correctly until several times checking of echocardiography. 28 of them had been misdiagnosed as dilated cardiomyopathy (DCM) in local hospitals. All but 2 subjects were inconsistent between echocardiography measurement and CMR. The ratio of N/C was 2,63±0,49 by CMR, and 2,55±0,43 by echocardiography. Conclusion. Echocardiography can be the first choice of NCC assessment for its advantages of being non-radiative, real-time, economic and characteristic. When the echocardiographic image is not typical in the early stage of NCC, a combination with CMR is necessary.
Highlights
Noncompaction cardiomyopathy (NCC) is a special and rare kind of inborn cardiomyopathy, which is known as the spongy myocardium or myocardial sinusoidal persistent state [1,2,3,4]
More attention had been paid to this condition, which resulted in an increased detection of NCC cases
Echocardiography Referring to the total echocardiographic times the patients had received since the disease onset, we found that 17 of the 56 patients had been diagnosed with NCC after the first survey in our institution, accounting for 30% of the total subjects
Summary
Noncompaction cardiomyopathy (NCC) is a special and rare kind of inborn cardiomyopathy, which is known as the spongy myocardium or myocardial sinusoidal persistent state [1,2,3,4]. It is characterized by excessive and prominent trabeculations associated with deep recesses that communicate with the ventricular cavity but not the coronary circulation [1,2,3,4]. NCC is thought to result from the arrest of myocardial compaction process during that period It is associated with other cardiac and systemic anomalies [6]. We retrospectively documented all clinical data and echocardiographic diagnosis of patients who were identified with NCC in our institution
Sign-in/Register to view highlights & summary Sign-in/Register to access full text options 
Free) 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call
