Temporal Fossa Ewing Sarcoma: Case Illustration

Abstract

Introduction: Ewing sarcomas of the skull are very rare neoplasms affecting typically children and adolescents. These tumors may mimic common skull base meningiomas but painful presentation is characteristic. Their local invasiveness raises the problematic of their management. Case History: We present the case of a 20-year-old woman who presented with a right temporal painful tumefaction. Her neurological examination revealed an isolated bilateral papilledema. MRI confirmed a right temporal fossa extra- and intradural mass extending to the sphenoidal sinus while body PET-scan was negative. The severe mass effect led to a rapid surgical subtotal removal not reaching the sphenoidal sinus extension. Postoperative neurological examination was normal. The patient underwent radiotherapy with both induction and adjuvant chemotherapy. Conclusion: Ewing sarcoma of the skull base should be considered in case of locally aggressive neoplasm especially when extradural extension is suspected. A maximal surgical removal is necessary followed by oncological treatment.