Syringocystadenoma Papilliferum of the Bony External Auditory Canal: A Rare Tumor in a Rare Location

Anastasija Arechvo,Svajunas Balseris,Irina Arechvo,Laura Neverauskiene

doi:10.1155/2013/541679

Anastasija Arechvo, Svajunas Balseris + Show 2 more

Open Access

https://doi.org/10.1155/2013/541679

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Abstract

Tumors originating from ceruminous glands are rare lesions of the external auditory canal. The lack of specific clinical and radiological signs makes their diagnosis challenging. We report the case of an exceptionally rare benign tumor, a syringocystadenoma papilliferum (SCAP), in an atypical location in the bony segment of the external auditory canal with uncommon clinical signs. The special traits of the case included the following: the most lateral component of the tumor was macroscopically cystic and a granular myringitis with an obstructing keratin mass plug was observed behind the mass. The clinical, audiological, radiological, and histological characteristics of the neoplasm are consequently presented. Intraoperative diagnosis of the epidermal cyst was proposed. The final diagnosis of SCAP was determined only by histological analysis after the surgical excision. The educational aspects of the case are critically discussed.

Highlights

Syringocystadenoma papilliferum (SCAP) was first described in the dermatological literature in the beginning of the 20th century as a “naevus syringadenomatosus papilliferus” [1]
We report the case of an exceptionally rare benign tumor, a syringocystadenoma papilliferum (SCAP), in an atypical location in the bony segment of the external auditory canal with uncommon clinical signs
According to the World Health Organization, the ceruminous gland neoplasms are currently classified as benign ceruminous adenoma, chondroid syringoma, SCAP and malignant adenocarcinoma, adenoid cystic carcinoma, and mucoepidermoid carcinoma [6]

Summary

Introduction

Syringocystadenoma papilliferum (SCAP) was first described in the dermatological literature in the beginning of the 20th century as a “naevus syringadenomatosus papilliferus” [1]. This type of tumor may arise in the external auditory canal (EAC). In 1894, Haugh described the first ceruminous gland tumor of the cartilaginous segment of the EAC [4]. Fewer than 150 case reports of ceruminous gland tumors originating in the EAC can be found in the literature [4]. Diagnostic modalities and the problem of differentiating SCAP from other benign and malignant masses of the EAC are critically discussed

Case Report

Discussion

Findings

Conflict of Interests