Synovial sarcoma of the vulva: a case report

Viren Asher,Gerhard Van Schalkwyk,Anish Bali

doi:10.1186/1752-1947-5-95

Viren Asher, Gerhard Van Schalkwyk + Show 1 more

Open Access

https://doi.org/10.1186/1752-1947-5-95

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Journal: Journal of Medical Case Reports	Publication Date: Mar 10, 2011
Citations: 21	License type: CC BY 2.0

Affiliation: Royal Derby Hospital

Abstract

IntroductionContrary to its name, synovial sarcoma does not arise from the synovial membrane but from multipotent stem cells and can present in any part of the body. Very few cases of vulval synovial sarcoma have been reported in the literature; we report on such a presentation. These tumors can present as painless lumps, which must be completely excised to give the best prognosis. Therefore the diagnosis of synovial sarcoma should always be kept in mind in the management of vulval masses, especially in young patients.Case presentationWe report the case of a 28-year-old Caucasian woman with synovial sarcoma of the vulva. Complete excision was possible in this case.ConclusionWe have presented a rare case of synovial sarcoma of the vulva, which can be easily confused with lipoma of the vulva. The management of this tumor requires referral to a cancer centre, with a multidisciplinary approach.

Highlights

Contrary to its name, synovial sarcoma does not arise from the synovial membrane but from multipotent stem cells and can present in any part of the body
Case presentation: We report the case of a 28-year-old Caucasian woman with synovial sarcoma of the vulva
We have presented a rare case of synovial sarcoma of the vulva, which can be confused with lipoma of the vulva

Summary

Introduction

Synovial sarcoma is the fourth most commonly occurring sarcoma, accounting for 7-8% of all sarcomas [1] It most frequently occurs in young adults, with up to 30% being manifested during the first two decades of life, and a median age of 13 years at presentation [2]. Clinical examination revealed a healthy woman with a well-defined deep mobile mass in her left labium majus. She underwent excision of the swelling under general anesthetic and the lump, which did not appear to be attached to adjoining structures, was dissected free from the underlying tissue. 1 & 2 30 and 37-year-old patients presented Excision of the lumps with painless mass on vulva. We have followed up our patient with clinical examinations and a chest X-ray every three months for the last three years, and there is still no evidence of recurrence

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Conclusion