Surgical resection of sequential thoracic aortic aneurysms in Wiskott–Aldrich syndrome

Abstract

Wiskott-Aldrich syndrome is a rare X-linked disorder. Vasculitis and aneurysm formation are extremely rare but potentially fatal complications of the disease. Aortitis and aneurysm formation seem to be progressive in patients with Wiskott-Aldrich syndrome. The risk of death from aneurysmal rupture in patients with Wiskott-Aldrich syndrome is high and hence surgery is required for resection of aneurysms. We report a case where a successful resection of a descending thoracic aneurysm was carried out in a patient who previously had undergone a composite root replacement for aortic root dilatation.