Abstract
Background: Fibrous dysplasia is an uncommon skeletal disorder in which normal bone and marrow are replaced with fibro-osseous tissue. The disease comprises 2.5% of all bone tumors and 7.5% of all benign bone neoplasm. It is the progressive, slowly developing disease and the optimum treatment remains unclear in many cases. Aim: In this study, the authors report their experience in the surgical treatment of four cases of craniofacial fibrous dysplasia. Cases presentation: The study involved 4 patients with craniofacial fibrous dysplasia. There were 3 men and a woman. The patients were 10, 17, 20 and 8 years old. No patient had a focal neurological deficit. The CT scan appearance was compatible with Fibrous dysplasia in all patients. The site of disease was frontal in one case and parietal in the other 3 cases. Cosmetic surgical treatment was performed in all patients. Cranioplasty was performed in one patient and planned for the other three. Conclusion: Fibrous Dysplasia is a benign slow growing disease that may cause as well as clinical symptom and aesthetical discomfort. Radical resection, if possible, is the only technique to obtain resolution of the disease.
Highlights
Fibrous dysplasia is an uncommon skeletal disorder in which normal bone and marrow are replaced with fibro-osseous tissue
Aim: In this study, the authors report their experience in the surgical treatment of four cases of craniofacial fibrous dysplasia
The computed tomography (CT) scan appearance was compatible with Fibrous dysplasia in all patients
Summary
The disease is classified into three variants: monostotic, polyostotic, and McCune-Albrigtht syndrome [3]. FD comprises 2.5% of all bone tumors and 7.5% of all benign bone neoplasm [5]. The monostotic form occurs most frequently and represents 75% of cases [3]. On computed tomography (CT) scan and radiography, the healthy bone is replaced by bone with a “ground-glass” appearance, with no visible trabecular pattern [5]. FD is the progressive, slowly developing disease and the optimum treatment remains unclear in many cases. Clinical observation is recommended in asymptomatic patients and surgery remains the mainstay of treatment if the disease affects normal life [8]. The authors report their experience in the surgical management of four cases of CFD
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