Abstract
Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a severe cardiac arrhythmogenic hereditary illness, which affects children and young adults with a structurally healthy heart. Its prevalence is of one case in 10 thousand inhabitants. It is a potentially fatal illness, part of the differential diagnosis of syncope in children. The present study has the purpose of relating the case of a child that, during the investigation of convulsive syncope, presented sudden death aborted due to CPVT and to describe the diagnosis difficulties of the case, comparing with data from the literature
Highlights
Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a severe cardiac arrhythmogenic hereditary illness that affects children and young adults with a structurally healthy heart
The possibility of CPVT must be taken into consideration when there is polymorphic adrenally-induced ventricular tachycardia, in the absence of any other cardiac structural or electric anormality[3,4]
Due to the advanced age of its presentation, generally between seven and 12 years of age, and due to the patients having hearts without structural alterations, many receive the wrong diagnosis of orthostatic dysregulation or epilepsy, delaying, this way, the treatment for CPVT5,11,12
Summary
Sudden Death by Catecholaminergic Polymorphic Ventricular Tachycardia in Children. Morte Súbita por Taquicardia Ventricular Polimórfica Catecolaminérgica em Criança. Isabella João Milan1,*, Fernando Mello Porto[2], Halim Cury Filho[2], Adão Bento de Lucena Neto[2], Jose Marco Nogueira Lima[2]
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