Successful Embolization of Type II Congenital Extrahepatic Portosystemic Shunt Using Amplatzer Septal Occluder and Amplatzer Vascular Plug II

Abstract

A 13-year-old boy with intermittent episodes of hematochezia, gradually progressive dyspnea, and cyanosis over the last decade showed an abnormal, tortuous, vascular channel along the left paravertebral region, with relatively small main portal vein and portal vein branches on ultrasound. Computed tomography angiography revealed bilateral inferior vena cava with a dilated tortuous vascular channel connecting the splenic vein cranially and the left internal iliac vein (IIV) caudally, suggesting type II congenital extrahepatic portosystemic shunt (Fig 1a–c).