STURGE-WEBER SYNDROME ASSOCIATED WITH CENTRAL SEROUS RETINOPATHY: A RARE CASE SCENARIO

Abstract

Aim: To report a rare case with Sturge-Weber Syndrome associated with central serous retinopathy. SWS is a rare sporadic genetic disease and diagnosis is primarily done by evaluating history, the presence of port-wine stain, and characteristic features on brain radio imaging. As no denitive treatment is available yet, patients are being treated by medical and surgical interventions for symptoms as well as for associated complications. Material And Methods: 18-year-old male presented with blurred vision and was found to have elevated intraocular pressure (IOP) and glaucomatous disc damage in the left eye. He also displayed capillary malformation (port-wine stain) on the same side of the face. IOP got reduced after prescribing a topical anti-glaucoma drug. This case exhibits a very rare occurrence of Sturge-Weber syndrome affecting the left side of the face associated with ipsilateral central serous retinopathy. The patient responded Result: well to the topical beta-blocker in the subsequent follow-up when the IOP was found to be well controlled. Central serous retinopathy also got reduced in 1 month with no changes in BCVA. Sturge-Weber syndrome is a Conclusion: rare phacomatosis that may present with central serous retinopathy