Steatocystoma multiplex - case report

Abstract

Steatocystoma multiplex is a rare, benign, sporadic or familial disorder (autosomal dominant mutation in Keratin 17). Diagnosis is based on clinical grounds: multiple cysts, localized in axilla, groin, neck, scrotum and proximal extremities. We describe a case of Steatocystoma multiplex in a 28 year old male patient with a family history of similar lesions.