Abstract
Background/aimHypoplastic left heart syndrome (HLHS) is a rare pathology with a very high mortality rate. The present study aimed to share our initial experience with the ductus arteriosus stenting procedure using the pulmonary trunk approach in the treatment of HLHS, as well as provide some technical suggestions and discuss complications and their management.Materials and methodsThe medical records of 9 neonates (age range: 1–8 days) with HLHS, who were operated on within a 12-month period, were reviewed retrospectively. Preprocedural planning was performed by computed tomography angiography and echocardiography. The operations were performed in a hybrid surgery room by interventional radiologists and pediatric vascular surgeons. Balloon-expandable stents were used in all of the operations.ResultsAll operations were successfully completed without any intraoperative mortality. All intraoperative complications were managed successfully during the stenting procedure.ConclusionStage 1 hybrid palliation for HLHS is a safe and effective procedure when several key points are kept in mind.
Highlights
Hypoplastic left heart syndrome (HLHS), which was first described by Lev in 1952 as hypoplasia of the aortic tract complexes, is characterized by hypoplasia of the aortic arcus and developmental failure of the left-sided heart chambers at varying degrees [1]
Prenatal diagnosis of HLHS enables the early infusion of prostaglandin, which in turn facilitates the maintenance of systemic cardiac output through the ductus arteriosus (DA) and improves survival rates after the first stage of palliative surgery when compared with postnatal diagnoses. [3]
The present study aimed to present the procedural outcomes of the stage 1 hybrid palliation and pulmonary trunk approach in the treatment of HLHS, as well as provide some practical key points and discuss complications and their management using the modified technical approach for stenting of the DA
Summary
Hypoplastic left heart syndrome (HLHS), which was first described by Lev in 1952 as hypoplasia of the aortic tract complexes, is characterized by hypoplasia of the aortic arcus and developmental failure of the left-sided heart chambers at varying degrees [1] Inadequate treatment of this pathology results in a decrease in life expectancy to 10% within the first month of life [2]. With recent advances in endovascular interventional technology, hybrid palliation has become popular as an alternative to the stage 1 Norwood procedure. This procedure can be used as an alternative to pretransplant palliation and
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
