Abstract
Spinal arachnoid cysts are benign and uncommon in children. The etiology may be congenital or traumatic. Despite the development of magnetic resonance in recent years, its findings are generally accidental. The most common symptoms are pain and progressive paraparesis, asymmetrical. Its appearance may be part of lymphedema distichiasis syndrome to be motivated by mutations in the FOXC2 gene transmitted as an autosomal dominant. A case of a girl with D3 ASIA C paraplegia is reported. The spine magnetic resonance revealed two posterior epidural spinal arachnoid cysts from D1-D2 to D8-D9 and from D12 to L2 and D6 and D8 myelopathy. Rehabilitation treatment program as well as surgical to evacuation of the cysts. Reviewing the clinical history, by the father, grandmother and cousin had spinal arachnoid cysts and lymphedema distichiasis syndrome respectively. A genetic study of girl, her brother and father confirms the FOXC2 gene mutation.
Highlights
Spinal extradural arachnoid cysts are rare lesions in children1
Multiple Spinal Arachnoid Cysts (SAC) occur between the ages of 9 and 14 and their location varies from the posterolateral region of the cervical spinal cord to the sacral, displacing it to the front [1,2,3,4,5,6]
We report the case of a girl with D3 ASIA C paraplegia secondary to dorsal SAC
Summary
Their finding is generally accidental, because rarely cause a spinal compression, the incidence has increased due to the development of Magnetic Resonance Imaging (MRI) [1,2] They usually are solitary lesions located in the dorsal region of the spinal cord [1,2]. We report the case of a girl with D3 ASIA C paraplegia secondary to dorsal SAC. In her family inherited syndrome is diagnosed. The vast majority are asymptomatic, when given symptoms most characteristic is the pain at level of the lesion, in cervical, lumbar and sacral region cyst, and progressive spastic or flaccid paraplegia, often symmetrical; usually related to spinal cord compression [3]. The most striking symptom was symmetric spastic paraplegia and severe impairment of proprioceptive sensitivity, made to orient diagnosis
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