Solitary Plexiform Neurofibroma of the Parotid Facial Nerves in a Child with NF1: Case Report and Review of Literature

Abstract

Plexiform neurofibromas (PNF) are benign tumors originating from peripheral nerve sheaths; generally associated with Neurofibromatosis Type 1 (NF1) usually involving a long segment of a major nerve trunk and extending into the nerve branches and they result in the so-called bag of worm’s appearance. The MRI features of neurofibromas are characteristic and can be helpful in the evaluation of a mass in a patient with known NF1.Theyhave mostly a predilection towards the limbs, in contract less than a dozen cases in all literature report a juxta-parotidien PNF.