Solitary fibrous tumor of the pleura with Doege-Potter syndrome.

Sara Waguaf,Mohamed Ridai,Souheil Boubia,Abdellah Fatene,Najat Id El Haj

doi:10.15342/atd.2021.470

Abstract

Solitary fibrous tumor of pleura (SFTP) is a rare tumor. Complete tumor resection is the curative treatment and the key to preventing recurrence. We present here the case of a 65-year-old female diagnosed with a Doege-Potter syndrome who underwent resection of pleural solitary fibrous tumor.

Highlights

Solitary fibrous tumor of the pleura (SFTP) is a rare neoplasm with mesenchymal cell origins
Hypoglycemia associated Solitary fibrous tumor of pleura (SFTP) is referred to as the Doege-Potter syndrome (DPS) and is caused by inappropriate secretion of an insulin-like growth factor II (IGF-II), a pattern seen in fewer than 5% of cases (1, 2, 3).Here, we described a case of malignant SFTP with DPS
A complete resection of the mass was performed with a good postoperative evolution including the disappearance of hypoglycemia.The patient was discharged on postoperative day 5

Summary

INTRODUCTION

Solitary fibrous tumor of the pleura (SFTP) is a rare neoplasm with mesenchymal cell origins. CASE PRESENTATION A 65-year-old woman with no particular medical history, was hospitalized with a complaint of syncopal episode associated with right chest pain. A chest X-ray showed a right dense, homogeneous, opacity (Figure 1). Chest computed tomography (CT) scan demonstrated a right large, well-circumscribed, homogeneous pleural mass measuring 17 * 13 * 12 cm (Figure 2). To determine the origin of this tumor, a transthoracic puncture was performed, revealing a pleural origin of the neoplasm. Right posterolateral thoracotomy through the seventh intercostal space was performed for the resection of the tumor. Surgical exploration revealed a large, wellcircumscribed encapsulated pleural mass measured 20 cm and weighed 2000 g (Figure 3). A complete resection of the mass was performed with a good postoperative evolution including the disappearance of hypoglycemia.The patient was discharged on postoperative day 5. There is no clinical or radiologic evidence of tumorrecurrence

Findings

DISCUSSION

CONCLUSION