Síndrome De Herlyn-Werner-Wunderlich: Relato De Caso

Abstract

Brief Description of the Purpose of the ReportThe Herlyn-Werner-Wunderlich syndrome usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. It consists of an important differential diagnosis in cases of dysmenorrhea, and should be properly treated before complications occur.Medical HistoryThe authors report a case of a 17 year old girl, a virgin, complaining of pain in the left iliac fossa with 15 days of evolution, exacerbated in the last 48 hours. Menarche at age 12. A pelvic and gynecological ultrasound showed absence of the left kidney, voluminous heterogeneous echogenic and well defined mass at the level of the vagina, with fine echoes in suspension and maximum diameter of 8 cm, allowing posterior acoustic enhancement, suggesting liquid nature, plus two uterine cavities.DiagnosisUltrasonography is the modality of choice for initial evaluation of suspected Müllerian malformations. Magnetic Resonance Imaging is the preferred method for the delineation of these uterine malformations.Discussion and Summary of the CaseThe Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterized by didelphys uterus, obstructed hemivagina and ipsilateral renal agenesis. Due to the close relationship between the development of the urinary and reproductive systems, renal malformations should be investigated in patients with Müllerian anomalies and vice versa. Brief Description of the Purpose of the ReportThe Herlyn-Werner-Wunderlich syndrome usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. It consists of an important differential diagnosis in cases of dysmenorrhea, and should be properly treated before complications occur. The Herlyn-Werner-Wunderlich syndrome usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. It consists of an important differential diagnosis in cases of dysmenorrhea, and should be properly treated before complications occur. Medical HistoryThe authors report a case of a 17 year old girl, a virgin, complaining of pain in the left iliac fossa with 15 days of evolution, exacerbated in the last 48 hours. Menarche at age 12. A pelvic and gynecological ultrasound showed absence of the left kidney, voluminous heterogeneous echogenic and well defined mass at the level of the vagina, with fine echoes in suspension and maximum diameter of 8 cm, allowing posterior acoustic enhancement, suggesting liquid nature, plus two uterine cavities. The authors report a case of a 17 year old girl, a virgin, complaining of pain in the left iliac fossa with 15 days of evolution, exacerbated in the last 48 hours. Menarche at age 12. A pelvic and gynecological ultrasound showed absence of the left kidney, voluminous heterogeneous echogenic and well defined mass at the level of the vagina, with fine echoes in suspension and maximum diameter of 8 cm, allowing posterior acoustic enhancement, suggesting liquid nature, plus two uterine cavities. DiagnosisUltrasonography is the modality of choice for initial evaluation of suspected Müllerian malformations. Magnetic Resonance Imaging is the preferred method for the delineation of these uterine malformations. Ultrasonography is the modality of choice for initial evaluation of suspected Müllerian malformations. Magnetic Resonance Imaging is the preferred method for the delineation of these uterine malformations. Discussion and Summary of the CaseThe Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterized by didelphys uterus, obstructed hemivagina and ipsilateral renal agenesis. Due to the close relationship between the development of the urinary and reproductive systems, renal malformations should be investigated in patients with Müllerian anomalies and vice versa. The Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterized by didelphys uterus, obstructed hemivagina and ipsilateral renal agenesis. Due to the close relationship between the development of the urinary and reproductive systems, renal malformations should be investigated in patients with Müllerian anomalies and vice versa.