Situs ambiguous-polysplenia syndrome: Torsion splenunculus – A rare cause of acute abdomen pain

Abstract

Situs ambiguous, also known as heterotaxy syndrome, is a rare congenital condition in which there is an abnormal positioning of internal organs of the chest and abdomen. Polysplenia (left isomerism) is a common association with it and hence called as “Situs Ambiguous-Polysplenia” syndrome. Torsion splenunculi is a rare complication associated with it. Herein, we report a case of splenunculi torsion in an adult with situs ambiguous associated with polysplenia.