Sinonasal Hemangiopericytoma In Adolescents: Histopathologic And Surgical Dilemma

Abstract

Sinonasal Hemangiopericytoma (HP) is a rare vascular tumor believed to derive from perivascular modified smooth muscle cells (pericytes). It comprises only one percent of all vascular neoplasms and approximately three percent of all soft tissue sarcomas1, 2. The majority of HPs occur in the trunk and lower extremities, with the head and neck being involved in only about 7.5-16 percent of cases3, 4. The majority of the cases involving the head and neck occur in the nasal cavity, paranasal sinuses, orbit, parotid gland, and the neck5,6,7. These tumors occur in all age groups with no sex predilection, and a peak incidence between the 5 and 6 decade8. Angiofibroma is a soft tissue vascular tumor that usually occurs in the nasopharynx or less frequently, in the posterior nasal cavity in adolescent males25. We report three cases of HPs occurring in adolescents, one in female & two in male's .In males they were resembling as angiofibroma on clinical presentation & radiologically ,where as in female patient it was mimicking as a fibrous tumour involving nasopharynx and paranasal sinuses.