Simultaneous repair for aortic incompetence with annuloaortic ectasia and pectus excavatum by modified Ravitch procedure with pectus bars in an adult patient with Marfan syndrome

Abstract

rence, even if this operation impaired the patient’s quality of life (bypass, valve replacement, and ventricular septal defect patch closure). Cases of cardiac transplantation to treat these fibromas have also been reported. However, subtotal resection seems to be the best therapeutic option when the size or location of the tumor makes total resection impossible. The risk of tumor regrowth seems to be relatively low. Several colleagues have described the absence of tumor progression at long-term follow-up, even if the number of cases reported is low. Finally, transplantation does not seem to be an acceptable option, even with voluminous fibromas; subtotal resection should be the treatment of choice. Even if it is widely accepted that fibromas should be totally resected because of their recurrence risk, subtotal surgical intervention might be an acceptable option when the volume or location of the tumor makes total resection a high-risk procedure.