Shoulder musculoskeletal changes present in Sprengel deformity: a scoping review protocol

Abstract

Introduction: Sprengel syndrome is a rare condition in which the scapula is located in an abnormally high position on the back. This condition occurs due to abnormal musculoskeletal development in the shoulder region during pregnancy. Objective: to verify in the literature which musculoskeletal changes in the shoulder complex are present in children with Sprengel syndrome. Methods: a scoping review of primary, observational or interventional studies will be carried out, as long as they report musculoskeletal changes in patients with Sprengel deformity. The study protocol was registered on the Prospero Platform (CRD42022381782). We will include children aged 5 to 10 years with Sprengel’s deformity (even if a longer period). Exclusion criteria: any other type of congenital comorbidity not associated with Sprengel’s deformity. The searches will be carried out in the following databases: Medical Literature Analysis and Retrieval System Online (Medline) via Pubmed, Excerpta Medica dataBASE (Embase) via Elsevier, Literatura Latino-Americana, Scientific Electronic Library Online (SciELO) and the Caribbean in Health Sciences (Lilacs) via the Virtual Health Library Portal, using relevant descriptors and synonyms. Two authors will extract the data independently and possible disagreements will be resolved with a third author. Evidence will be presented according to the Joanna Briggs Institute (JBI) method. Expected results: Map the musculoskeletal changes in the shoulder complex present in Sprengel’s deformity to assist professionals in clinical practice and support future studies on this condition. Keywords: Sprengel deformity; congenital diseases; musculoskeletal syndromes.