Severe Fatal Pulmonary Hypertension in Newborn with Idiopathic Arterial Calcification

Abstract

Idiopathic congenital calcification of the great vessels is a rare genetic disorder affecting the infants during first months of live causing fatal complications [13] due to generalized calcification of the moderate to large vessels leading to decrease elasticity and occlusion of these vessels [4]. We prescribe 2 days old boy with respiratory distress and mild central cyanosis, his echocardiography reveal a calcified aorta and pulmonary arteries with sever pulmonary hypertension that was diagnosed later as idiopathic congenital arterial calcification of infancy.